Sturge-Weber syndrome with posterior fossa involvement.

Sturge-Weber syndrome, encephalotrigeminal angiomatosis, is a neurocutaneous disorder characterized by a facial cutaneous vascular nevus, seizures, mental retardation, hemiplegia, homonymous hemianopia, and buphthalmos or glaucoma (1). The clinical findings are related to vascular anomalies of the face, ocular choroid, and leptomeninges. The imaging findings in Sturge-Weber syndrome may include cerebral calcifications, cerebral atrophy, choroid plexus anomalies, pial and/ or cortical enhancement, and prominent deep-draining veins. The leptomeningeal vascular anomaly is usually located in the anterior occipital, posterior parietal, and temporal cerebrum.